心房颤动机制研究进展--细胞核孔复合物与跨核运输障碍.ppt
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1、心房颤动机制研究进展-细胞核孔复合物与跨核运输障碍 Still waters run deep.流静水深流静水深,人静心深人静心深 Where there is life,there is hope。有生命必有希望。有生命必有希望故事的开始:故事的开始:常染色体隐性遗传房颤家常染色体隐性遗传房颤家系系21 1-57 family members-32 males-25 females-5 living generations-Age:3 m-93 y-Autosomal recessive inheritance pattern-7 consanguineous marriagesAn Int
2、eresting FamilyCirculation,2004Oberti et al.Circulation,2004;110:3753-3759Proband V:11-Chronic AF-QTc=0.42 s-Delivered by caesarean section due to fetal tachycardia,HR of 250 bpm,atrial fibrillation and atrial flutter-Echo at day 2:marked dilatation of both atria,EF 52%-EP at 1 m detected AF,ablatio
3、n of AV node-Pacemaker Echo at 2 m:mild atrial dilatation,normal EF 52%-Died suddenly at 15 mOberti et al.Circulation,2004;110:3753-3759Patient VI:2-Chronic AF-QTc=0.40 s-HR=125 bpm with digoxin and propafenoneEcho at 15 m:normal-Died suddenly at 19 mOberti et al.Circulation,2004;110:3753-3759Patien
4、t V:9-Atrial flutter-Delivered by C section due to fetal tachycardia-Born with supraventricular tachycardia-ECG at 24 d:atrial flutter,HR=200 bpm-Echo at 24 d:normal-Later Echo:mild dilatation of left ventricle and left atria-Died suddenly at 3 mOberti et al.Circulation,2004;110:3753-3759Patient V:1
5、0-Born with atrial tachycardia-Echo:normal-Died suddenly at 2 mPatient VI:1-Born with atrial tachycardia-Electrical conversion at 20 d-Echo at 1 m:normal-Died suddenly at 18 mPatient VI:3-Born with AF and atrial tachycardia on Feb.14,2007-In sinus rhythm on propafenone,propranolo,aspirinFamily membe
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- 关 键 词:
- 心房 颤动 机制 研究进展 细胞核 复合物 运输 障碍
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